Dolor pélvico cíclico en paciente con síndrome de Mayer Von Rokitansky-Küster-hauser, a propósito de un caso

Luisa Camacho González; Josimar Rivas; María Pérez; Priscila Rodríguez

doi:10.37910/RDP.2026.15.2.e461

Authors

Luisa Camacho González Ginecología Infantil y Juvenil, Hospital de Niños “Dr. José Manuel de los Ríos”
Josimar Rivas Ginecología Infantil y Juvenil, Hospital de Niños “Dr. José Manuel de los Ríos”
María Pérez Ginecología Infantil y Juvenil, Hospital de Niños “Dr. José Manuel de los Ríos”
Priscila Rodríguez Ginecología Infantil y Juvenil, Hospital de Niños “Dr. José Manuel de los Ríos”

DOI:

https://doi.org/10.37910/RDP.2026.15.2.e461

Keywords:

Malformación Útero-Vagina, Dolor Pélvico, Derivado Mülleriano

Abstract

Mayer von Rokitansky Kuster Hauser syndrome is a uterine-vaginal malformation with normal development of secondary sexual characteristics. Diagnosis is often made during adolescence, with the cardinal symptom being the absence of menstruation. However, cyclical pelvic pain is another, albeit rare, reason for consultation. We report the case of a 13-year-old adolescent who complained of cyclical pain located in the hypogastrium and pelvic region. Based on the physical examination findings, an ultrasound was performed, revealing a functioning Müllerian derivative and an ectopic kidney, and she was taken to the operating table. Knowledge of the syndrome and its variants is essential for accurate diagnosis and proper management, due to the implications for the physical and emotional health of the patient and her family.

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